Sebaceous carcinoma is a rare cutaneous malignancy. It occurs most frequently in the sixth to eighth decades of life and is most commonly located peri-orbitally. Extra-ocular sebaceous carcinoma is less common but has the same age distribution. In general, the prognosis is better in extra-ocular sebaceous carcinoma. In the literature, only 12 cases of pediatric sebaceous carcinoma have been reported, and only 2 of these cases were extra-ocular. We report the case of a 6-year-old boy who had a lesion on the left elbow for a year. A biopsy of the lesion was performed. The pathologic specimen was reviewed by three different pathologists in United States, all of whom concurred with the diagnosis of sebaceous carcinoma. The patient underwent re-excision of the lesion with wide margins and will be followed up periodically. In addition to this case report, a general review of the literature on sebaceous carcinoma will be provided, with emphasis on pediatric and extra-ocular cases, including etiology, risk factors, management, and follow-up. This is only the third case of extra-ocular pediatric sebaceous carcinoma reported in literature, and the youngest patient reported.
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