PATIENTS AND METHODS: A retrospective study was done for a total of 9 patients with neurofibromatosis type I in head and neck area. The age to start surgical intervention was from 2 months to 67 years. The mean follow-up time was 38 months (2months to 8 years). Serial pictures, image study and facial expressions were record.
RESULTS: (1) For facial contour, early and multiple surgical interventions could avoid severe asymmetry as well as distortion of mandible which are difficult to correct, in contrast to the patients operated late. (2) For the facial nerve function, maximal tumor excision and identification of facial nerve with microscope can reduce tumor-compression injury and result in better facial expression.
CONCLUSION: Close observation and early operation for neurofibroma will be the tendency of treatment in the future. If necessary, repetitive operation can be done with guidance of suture marked around the facial nerve branch.